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IgG4-related systemic disease and lymphoplasmacytic aortitis
Arthritis & Rheumatism, 10/05/09
Stone JH et al. – This case offers new potential considerations for short– and long–term management of noninfectious aortitis, because of the frequent good response of IgG4–related systemic disease to glucocorticoid treatment without additional therapy. Treatment of the aortitis may prevent progression of the IgG4–related systemic disease to involvement of other organs. IgG4–related systemic disease should be considered in all patients with aortitis judged to be of unknown etiology.
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