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Perfusion SPECT Findings in a Suspected Case of Rasmussen Encephalitis
Journal of Neuroimaging, 10/07/09
Tessonnier L et al. – The authors report the case of a 35–year–old who was referred for brain perfusion single photon emission computed tomography (SPECT) for pharmacoresistant epilepsy. Rasmussen syndrome is a rare unilateral devastating disease with childhood onset that can also occur in adulthood, characterized by intractable epileptic seizures associated with progressive neurological deterioration and unilateral progressive atrophy. Brain perfusion SPECT can speed up the diagnosis when exhibiting a strictly unilateral hemispheric hypoperfusion in such a clinical context. It can also guide brain biopsy in cases of inconclusive MRI.
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