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Articles: Cystic Fibrosis



Latest () Month's Top Read  
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Pulmonary vascular dysfunction in end-stage cystic fibrosis: Role of NF-kB and endothelin-1
European Respiratory Journal, 05/26/09
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Mutations in the amiloride-sensitive epithelial sodium channel in patients with cystic fibrosis-like disease
Human Mutation, 05/26/09
Hypoventilation in Cystic Fibrosis
Seminars in Respiratory and Critical Care Medicine, 05/21/09
Treatment of Acne with Oral Isotretinoin in Patients with Cystic Fibrosis
BMJ - Archives of Diseases in Childhood, 05/21/09
Real-time, once-daily monitoring of symptoms and FEV1 in cystic fibrosis patients – A feasibility study using a novel device
The Clinical Respiratory Journal, 05/20/09
Prevalence and clinical significance of autoantibodies in 144 adults with cystic fibrosis
European Respiratory Journal, 05/20/09
Iron-binding compounds impair Pseudomonas aeruginosa biofilm formation, especially under anaerobic conditions
Journal of Medical Microbiology, 05/19/09
Determination of the Minimal Clinically Important Difference Scores for the Cystic Fibrosis Questionnaire-Revised Respiratory Symptom Scale in Two Populations of Patients With Cystic Fibrosis and Chronic Pseudomonas aeruginosa Airway Infection
Chest, 05/19/09
Primary ciliary dyskinesia: prospects for new therapies, building on the experience in cystic fibrosis
Paediatric Respiratory Reviews, 05/19/09
Loss of CFTR results in reduction of histone deacetylase 2 in airway epithelial cells
Lung Cellular and Molecular Physiology, 05/15/09
Increased prevalence of risk factors for morbidity and mortality in the US Hispanic CF population
Pediatric Pulmonology, 05/14/09
Improvement after Angioplasty and Stenting of Pulmonary Arteries Due to Sarcoid Mediastinal Fibrosis
Heart, Lung, and Circulation, 05/14/09
Mucoid Inquilinus limosus in a young adult with cystic fibrosis
Pediatric Pulmonology, 05/13/09
Epigallocatechin-3-gallate augments antioxidant activities and inhibits inflammation during bleomycin-induced experimental pulmonary fibrosis through Nrf2–Keap1 signaling
Pulmonary Pharmacology and Therapeutics, 05/12/09
Qualitative aspects of breathlessness in health and disease
Thorax, 05/11/09    Evidence Based Medicine
IL1B polymorphisms modulate cystic fibrosis lung disease
Pediatric Pulmonology, 05/11/09
Statistical limitations of percent ideal body weight as measure for nutritional failure in patients with cystic fibrosis
Journal of Cystic Fibrosis, 05/11/09
Systemic colistin use in children without cystic fibrosis: a systematic review of the literature
International Journal of Antimicrobial Agents, 05/08/09
An overview of international literature from cystic fibrosis registries: 1. Mortality and survival studies in cystic fibrosis
Journal of Cystic Fibrosis, 05/08/09
Early anti-pseudomonal acquisition in young patients with cystic fibrosis: Rationale and design of the EPIC clinical trial and observational study,
Contemporary Clinical Trials, 05/08/09

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Indexed Journals: Chest, Thorax, American Journal of Respiratory and Critical Care Medicine more...
165 Available Pages
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