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Necrotizing Sarcoid Granulomatosis
Clinical Pulmonary Medicine, 09/16/08
Barreiro TJ et al. - Necrotizing sarcoid granulomatosis is a rare disorder, whose etiology and pathogenesis are a topic of great debate. Diagnosis is often mistaken for "typical" sarcoid, hypersensitivity pneumonitis, lymphoid granulomatosis, or Wegener granulomatosis. The disease occurs in the late forties and predominately in women. Extrapulmonary involvement is rare. Symptoms may be absent or mimic malignancy. Biopsy is needed for diagnosis. There is no standard treatment. Recommendations include steroids, observation, and surgical resection for localized disease.
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