Juxtarenal Wilms Tumor in an Adolescent
Gordetsky J et al. – A 17–year–old boy presented for evaluation of an abdominal mass. Imaging revealed a 12.5–cm left upper pole renal mass. Biopsy demonstrated a malignant neoplasm consistent with blastemal–type Wilms tumor. The patient received neoadjuvant chemotherapy followed by laparoscopic radical nephrectomy. Examination revealed an unremarkable kidney uninvolved by tumor abutted by a 7.3 cm encapsulated mass. Histology revealed a triphasic Wilms tumor with favorable histology. This tumor was classified as a juxtarenal Wilms tumor, a rare form of extrarenal Wilms tumor, with only 7 cases described in the literature.