Priapism in an Infant With Sickle Cell Trait After Cardiac Transplant
Bacsu CD et al. – The authors report a case of priapism in a 6–month–old boy of African descent who had been receiving intravenous sildenafil, a phosphodiesterase–5 inhibitor. An orthotopic cardiac transplantation had been performed at 6 months of age, 2 months after he had received a Berlin heart. The pre–, peri–, and postoperative care required multiple transfusions, and postoperative pulmonary hypertension required treatment with intravenous sildenafil. He developed a series of prolonged, semitumescent erections that resolved spontaneously without the need for urologic intervention. Subsequent investigations revealed he was a carrier of a sickle cell gene.