Unusual Clinical Presentation of Rare Adult Survivors With a Missing Pulmonary Valve Associated With a Missing Left Pulmonary Artery
Pediatric Cardiology, 08/20/2012
Sivakumar K et al. – This report describes two adult natural survivors with this rare association who presented with extremely unusual unreported clinical features. The aneurysmally dilated main pulmonary artery was compressed on the left coronary ostium, causing angina in the first patient. The second patient had recurrent ventricular tachycardia originating from the dilated thinned out right ventricular outflow tract. Both patients had successful surgical correction with valved xenograft conduits.