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Diffuse mesangial sclerosis Report of two cases Full Text
Indian Journal of Nephrology, 08/02/2012
Vankalakunti M et al. – Diffuse mesangial sclerosis (DMS) is a rare cause of nephrotic syndrome in the infantile and childhood period. DMS is a phenotypic expression of syndromic entities such as WAGR syndrome, Denys Drash syndrome, Pierson syndrome, Frasier syndrome, or Galloway–Mowat syndrome. The authors report two cases of DMS, one presenting in first year of life and another in second decade of life. Both of them had fatal outcome. Recognition of the disease is very important in modifying the management of patient and active surveillance of family members.