Pulmonary Interstitial Glycogenosis: An Unrecognized Etiology of Persistent Pulmonary Hypertension of the Newborn in Congenital Heart Disease
Pediatric Cardiology, 06/04/2012
Radman MR et al. – The authors report the second and third patients with Pulmonary interstitial glycogenosis (PIG) associated with CHD. Because histologic examination is required to establish the diagnosis, they speculate that PIG, although rare, may be underrecognized in neonates presenting with pulmonary hypertension of the newborn (PPHN) in the setting of CHD.