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Protein-energy malnutrition as the first manifestation of cystic fibrosis in infancy
Pediatrics International, 10/01/09
Fustik S et al. – PEM is a common manifestation of CF in infancy. Early infant age, breast–feeding, impaired liver function and the presence of severe cystic fibrosis transmembrane conductance regulator mutations are predisposing factors for the development of PEM.
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