Clinical Features and Outcome of Acute Exacerbation of Interstitial Pneumonia: Collagen Vascular Diseases-Related versus Idiopathic
Respiration, 09/09/2011
Tachikawa R et al. – Clinical features and outcome in acute exacerbation (AE) of interstitial pneumonia associated with collagen vascular diseases (CVD–IPs) were similar, if not identical, to those of interstitial pneumonias (IIPs), having a significant impact on the clinical course. Acute exacerbation (AE) of advanced IPF with typical radiologic features seems to have higher mortality compared with other forms of IP.






