Senft C et al. - In this paper, we report on the case of a patient with an unexpected and difficult-to-diagnose PPTID. A 2.2 × 2.2-cm midline mass within the posterior part of the third ventricle with consecutive obstructive hydrocephalus was found in a 44-year-old man presenting with diplopia and gait disturbances. There was no clear connection of the tumor to the pineal gland. Differential diagnosis included all intraventricular and midline tumors, therefore a biopsy was taken. Preliminary histopathological diagnosis was germinoma or primitive neuroectodermal tumor, and the tissue sample was reexamined by a referential neuropathological institute. Final diagnosis was PPTID. We recommend surgical removal of PPTID, preferably in toto whenever the size of the tumor permits that kind of excision.