The prevalence of early repolarization in patients with noncompaction cardiomyopathy presenting with malignant ventricular arrhythmias

Journal of Cardiovascular Electrophysiology, 05/16/2012

There is a high prevalence of ER in noncompaction cardiomyopathy (NCCM) patients, especially in those who present with malignant ventricular arrhythmias.


  • Authors analyzed prospective data from this NCCM registry including 84 patients, median age: 40 (3–79) years.


  • Fourteen patients (17%) initially presented with sustained VT (n = 5) or VF (n = 9) and 70 (83%) with heart failure or else.
  • After the exclusion of 20 patients with the left bundle branch block, 25 (39%) NCCM patients had ER; 3 (6%) located in inferior leads, 14 (27%) in lateral leads, and 8 (15%) in both.
  • None had ER in leads V1 to V3.
  • In those presenting with VT/VF, 9/12 (75%) had ER (2 in inferior leads, 3 in lateral leads and 4 in both), versus 16/52 (31%) in the other patients (P = 0.02).
  • If the NCCM population was dichotomized according to the presence or absence of ER, the long–term outcome for VT/VF appeared worse in the ER positive patients (P = 0.05).

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